Giant Omphalocele With Complete Herniation of Left Liver Lobe.

Femal baby born at 39th gestation week by cesarean section, birth weight 2900 gr. Diagnosis of giant omphalocele with herniation of bowel loops and liver was done at 22th week of pregnancy. Amniocentesis no revealed genetic anomalies, and at fetal RMN it was not appreciated cardiovascular, renal or other gastrointestinal abnormalities. No polidramnios complicated pregnancy.

Immediately at birth, baby was admitted to adjoninig operation room, so to reduce risk of transport inside the hospital. Giant omphalocele with erniation of bowel loops and left lobe of liver was confirmed. (Fig. A) Amniotic sac was excised and replaced with a silos mesh of Goretex and then closed over time. (Fig. B)

Progressive reduction of herniated viscera was achieved in four weeks in complete sedation, so we obtained an abdominal defect no more 1 cm of diameter and complete reduction of entire liver in the abdominal cavity (Fig. C). To this time, a definitive reconstruction of abdominale defect was done. (Fig. D)